The intestinal absorption defect in cystinuria
نویسندگان
چکیده
منابع مشابه
Intestinal absorption of an arginine-containing peptide in cystinuria.
Separate tolerance tests involving oral intake of the dipeptide, L-arginyl-L-aspartate, and of a corresponding free amino acid mixture, were carried out in a single type 2 cystinuric patient. Absorption of aspartate was within normal limits, whilst that of arginine was normal after the peptide but considerably reduced after the amino acid mixture. The results are compared with the increments of...
متن کاملIntestinal absorption of cystine and cysteine in normal human subjects and patients with cystinuria.
1. An intestinal perfusion technique has been used to study absorption in uivo of L-cystine and L-cysteine in six normal human subjects and three patients with homozygous cystinuria. 2. No significant absorption of L-cystine was detected during perfusion of the cystinuric patients, whereas L-cysteine absorption was normal. These results imply that L-cystine and L-cysteine are normally absorbed ...
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T.K., a female, was born after full term and spontaneous delivery, weighing 2,260 g. Her parents were healthy and not consanguineous. There was no sibling. The patient was breast fed and appeared to be healthy until 6 months of age, when the parents wondered if she might be mentally retarded. Even beyond one year of age she could neither stand nor sit alone. There was no history of convulsions ...
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Desferroxamine (Desferal) is used tochelate iron in thalassemia, a disease of very high prevalence in various parts of lran. We have investigated intestinal zinc absorption in Desferal-treated rats which, in pilot experiments, showed low serum levels of both iron and zinc. Intraperitoneal administration of ten 0.5 g doses of Desferal (one injection every other day) to male rats produced sev...
متن کاملAn Inborn Defect of Intestinal Absorption of Certain Monosaccharides.
Since 1958 defective digestion of the disaccharide sugars has received increasing attention and hereditary congenital deficiencies of the enzymes, lactase, sucrase, and isomaltase, have been very convincingly demonstrated both clinically and by methods which estimate enzyme activity in small intestinal mucosa. The unhydrolysed and therefore predominantly unabsorbed disaccharide gives rise to di...
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ژورنال
عنوان ژورنال: Gut
سال: 1961
ISSN: 0017-5749
DOI: 10.1136/gut.2.4.323